Tetralogy of Fallot
With pulmonic stenosis iiiim IIIII
With pulmonic atresia
Complex defect with ventricular septal defect, infundibular and usually valvular right ventricular outflow obstruction, mal-rotation of the aorta, and right-to-left shunting at ventricular septal level.
General. Variable cyanosis, increasing with activity
Location. Mid-to-upper left sternal border. If pulmonary atresia, there is no systolic murmur but the continuous murmur of ductus arteriosus flow at upper left sternal border or in the back.
Radiation. Little, to upper left sternal border, occasionally to lung fields
Intensity. LTsually Grade III-IV
Qitality. Midpeaking, systolic ejection
The pulmonary closure sound is usually not heard. May have abrupt hypercyanotic spells with sudden increase in cyanosis, air hunger, altered level of awareness
Failure to gain weight with persistent and increasingly severe cyanosis
Long-term persistence of cyanosis accompanied by clubbing of fingers and toes
Persistent hypoxemia leads to polycythemia, which will accentuate the cyanosis.
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Your heart pumps blood throughout your body using a network of tubing called arteries and capillaries which return the blood back to your heart via your veins. Blood pressure is the force of the blood pushing against the walls of your arteries as your heart beats.Learn more...